Sturge-Weber syndrome consists essentially of a vascular anomaly of the skin of the face, in the area served by the trigeminal nerve, associated with a presumed intracranial vascular anomaly. Frequent associated clinical findings are focal or generalized convulsion, ocular anomaly, contralateral hemiplegia, and mental retardation.

This is a case report of four typical Sturge-Weber syndrome in which data were sufficient establish the diagnosis.