Pneumothorax Associated with Noninvasive Intermittent Positive Pressure Ventilation in Duchenne Muscular Dystrophy: A case report.

, Baek, Jong Hoon; , Kang, Seong Woong; , Choi, Won Ah; , Lee, Soon Kyu

Case Report

Journal of the Korean Academy of Rehabilitation Medicine 2009;33(6):735-738.

Baek, Jong Hoon , Kang, Seong Woong , Choi, Won Ah , Lee, Soon Kyu

Department of Rehabilitation Medicine and Rehabilitation, Institute of Muscular Disease, Yonsei University College of Medicine, Korea. reedlove37@yuhs.ac

두시엔느 근디스트로피 환자에서 비침습적 환기보조 중 발생한 기흉−증례 보고−

백종훈, 강성웅, 최원아, 이순규

연세대학교 의과대학 재활의학교실 및 근육병 재활연구소

Abstract

Duchenne muscular dystrophy (DMD) is a severe X-linked recessive disorder characterized by rapid progression of muscle wasting and weakness. Long term noninvasive intermittent positive pressure ventilation (NIPPV) is an important treatment for neuromuscular patients with chronic respiratory failure. NIPPV is easy to administer and life-threatening complications are rare. We report two cases of pneumothorax associated with long term NIPPV in DMD. Given the increasing utilization of chronic NIPPV, we suggest that caregivers and patients must be aware of this potentially life-threatening complication. (J Korean Acad Rehab Med 2009; 33: 735-738)

Key Words: Duchenne muscular dystrophy, NIPPV, Pneumothorax