Juvenile Muscular Atrophy of the Upper Limb (Hirayama Disease): A case report.

, Lee, Hyun Kyung; , Kim, Dong Hyuk; , Jeon, Pyeong Sik; , Lee, Sung Hoon; , Kang, Eun Young; , Kim, Se Jong

Case Report

Journal of the Korean Academy of Rehabilitation Medicine 2004;28(4):387-391.

Lee, Hyun Kyung , Kim, Dong Hyuk , Jeon, Pyeong Sik , Lee, Sung Hoon , Kang, Eun Young , Kim, Se Jong

¹Department of Rehabilitation Medicine, Kwangju Christian Hospital, Korea. dirzahlee@hanmail.net
²Department of Radiology, Kwangju Christian Hospital, Korea.

비진행성 연소성 원위부 상지 근위축(Hirayama 질환)⁣증례 보고⁣

이현경, 김동혁, 전평식, 이성훈, 강은영, 김세종¹

광주기독병원 재활의학과, ¹진단방사선과

Abstract

Hirayama disease is characterized by focal amyotrophy of the upper limb associated with unilateral or asymmetric bilateral muscle weakness. It occurs in young men in their late teens or early twenties. Repeated or sustained neck flexion is thought to be a cause of the disease. It is important to prevent the progression of the disease through early recognition and management. We reported a patient with Hirayama disease in order to review the typical clinical, electrodiagnostic and radiological findings of Hirayama disease. (J Korean Acad Rehab Med 2004; 28: 387-391)

Key Words: Hirayama disease, Focal amyotrophy, Neck flexion